A practical approach to children with phaeochromocytomas and paragangliomas

Authors

  • L Strauss University of the Witwatersrand

Abstract

Phaeochromocytoma (PCC) and paraganglioma (PGL) are rare chromaffin cell tumours which secrete catecholamines and form part of the family of neuroendocrine tumours. They are responsible for 0.5–2% of cases of secondary hypertension in paediatrics and although rare, are potentially lethal. The presentation of hypertension in these patients is characteristic, and the treatment is definitive.1 Phaeochromocytoma and paragangliomas (PPGLs) have a reported annual incidence of two to five cases per million, of which only 10% occur in children.2

Author Biography

L Strauss, University of the Witwatersrand

Department of Anaesthesia Chris Hani Baragwanath Academic Hospital University of the Witwatersrand.

Downloads

Published

2018-05-28

Issue

FCA Anaesthetic Refresher Course 2018

Section

FCA Refresher Course

License

By submitting manuscripts to SAJAA, authors of original articles are assigning copyright to the SA Society of Anaesthesiologists. Authors may use their own work after publication without written permission, provided they acknowledge the original source. Individuals and academic institutions may freely copy and distribute articles published in SAJAA for educational and research purposes without obtaining permission.

The work is licensed under a Creative Commons Attribution-Non-Commercial Works 4.0 South Africa License. The SAJAA does not hold itself responsible for statements made by the authors.